Annotation Detail

Information
Associated Genes
MECP2
Associated Variants
MECP2 p.Arg145Cys (p.R145C) ( ENST00000303391.11, ENST00000407218.5, ENST00000415944.4, ENST00000453960.7, ENST00000628176.2 )
MECP2 p.Arg145Cys (p.R145C) ( ENST00000453960.7, ENST00000303391.11, ENST00000407218.5, ENST00000415944.4, ENST00000628176.2 )
Associated Disease
intellectual disability
Source Database
ClinVar
Description
NM_001110792.2(MECP2):c.433C>T (p.Arg145Cys) AND Intellectual disability
ClinVar Allele ID
26848
ClinVar RefSeq Alternation Syntax
NM_001386139.1:c.-164C>T
ClinVar RefSeq Alternation Syntax
NM_001369392.2:c.118C>T
ClinVar RefSeq Alternation Syntax
NM_001110792.2:c.433C>T
ClinVar RefSeq Alternation Syntax
NM_004992.4:c.397C>T
ClinVar RefSeq Alternation Syntax
NM_001386138.1:c.-164C>T
ClinVar RefSeq Alternation Syntax
NM_001369391.2:c.118C>T
ClinVar RefSeq Alternation Syntax
NM_001386137.1:c.-164C>T
ClinVar RefSeq Alternation Syntax
NM_001369393.2:c.118C>T
ClinVar RefSeq Alternation Syntax
NM_001316337.2:c.118C>T
ClinVar RefSeq Alternation Syntax
NM_001369394.2:c.118C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-04-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001257757
ClinVar Disease
Intellectual disability
Observed Origin Sample
de novo
Drugs