Annotation Detail

Information
Associated Genes
ABCG5 ABCG8
Associated Variants
ABCG5 p.Arg50Cys (p.R50C) ( ENST00000405322.8 )
ABCG5 p.Arg50Cys (p.R50C) ( ENST00000405322.8 )
Associated Disease
Sitosterolemia 1
Source Database
ClinVar
Description
NM_022436.3(ABCG5):c.148C>T (p.Arg50Cys) AND Sitosterolemia 1
ClinVar Allele ID
271030
ClinVar RefSeq Alternation Syntax
NM_022436.3:c.148C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2018-01-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001094756
ClinVar Disease
Sitosterolemia 1
Observed Origin Sample
germline
Drugs