Annotation Detail

Information
Associated Genes
ERCC4
Associated Variants
ERCC4 p.Pro379Ser (p.P379S) ( ENST00000682617.1, ENST00000311895.8 )
ERCC4 p.Pro379Ser (p.P379S) ( ENST00000311895.8, ENST00000682617.1 )
Associated Disease
Xeroderma pigmentosum, group F Fanconi anemia complementation group Q Cockayne syndrome
Source Database
ClinVar
Description
NM_005236.3(ERCC4):c.1135C>T (p.Pro379Ser) AND multiple conditions
ClinVar Allele ID
137887
ClinVar RefSeq Alternation Syntax
NM_005236.3:c.1135C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2024-01-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001083882
ClinVar Disease
Xeroderma pigmentosum, group F
ClinVar Disease
Cockayne syndrome
ClinVar Disease
Fanconi anemia complementation group Q
Observed Origin Sample
germline
Drugs