Annotation Detail

Information
Associated Genes
TFR2
Associated Variants
TFR2 p.Arg455Gln (p.R455Q) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
TFR2 p.Arg455Gln (p.R455Q) ( ENST00000223051.8, ENST00000431692.5, ENST00000462107.1 )
Associated Disease
Hereditary hemochromatosis
Source Database
ClinVar
Description
NM_003227.4(TFR2):c.1364G>A (p.Arg455Gln) AND Hereditary hemochromatosis
ClinVar Allele ID
20422
ClinVar RefSeq Alternation Syntax
NM_003227.4:c.1364G>A
ClinVar RefSeq Alternation Syntax
NM_001206855.3:c.851G>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2024-01-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001081144
ClinVar Disease
Hereditary hemochromatosis
Observed Origin Sample
germline
Drugs