Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Pro1380Leu (p.P1380L) ( ENST00000370225.4 )
ABCA4 p.Pro1380Leu (p.P1380L) ( ENST00000370225.4 )
Associated Disease
Retinal dystrophy
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.4139C>T (p.Pro1380Leu) AND Retinal dystrophy
ClinVar Allele ID
22943
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.3917C>T
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.4139C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-08-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001075868
ClinVar Disease
Retinal dystrophy
Observed Origin Sample
germline
Drugs