Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Arg2107Cys (p.R2107C) ( ENST00000370225.4 )
ABCA4 p.Arg2107Cys (p.R2107C) ( ENST00000370225.4 )
Associated Disease
Retinal dystrophy
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.6319C>T (p.Arg2107Cys) AND Retinal dystrophy
ClinVar Allele ID
623815
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.6319C>T
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.6097C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-03-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001074913
ClinVar Disease
Retinal dystrophy
Observed Origin Sample
germline
Drugs