Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Glu1122Lys (p.E1122K) ( ENST00000370225.4 )
ABCA4 p.Glu1122Lys (p.E1122K) ( ENST00000370225.4 )
Associated Disease
Retinal dystrophy
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.3364G>A (p.Glu1122Lys) AND Retinal dystrophy
ClinVar Allele ID
39174
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.3142G>A
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.3364G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-06-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001073572
ClinVar Disease
Retinal dystrophy
Observed Origin Sample
germline
Drugs