Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Pro76_Gln91del (p.P76_Q91del) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
PRNP p.Pro76_Gln91del (p.P76_Q91del) ( ENST00000379440.9, ENST00000424424.2, ENST00000430350.2, ENST00000457586.2 )
Associated Disease
Huntington disease-like 1
Source Database
ClinVar
Description
NM_000311.5(PRNP):c.180_227del (p.60_67PHGGGWGQ[2]) AND Huntington disease-like 1
ClinVar Allele ID
848464
ClinVar RefSeq Alternation Syntax
NM_001271561.3:c.91_138del
ClinVar RefSeq Alternation Syntax
NM_183079.4:c.180_227del
ClinVar RefSeq Alternation Syntax
NM_001080121.3:c.180_227del
ClinVar RefSeq Alternation Syntax
NM_000311.5:c.180_227del
ClinVar RefSeq Alternation Syntax
NM_001080123.3:c.180_227del
ClinVar RefSeq Alternation Syntax
NM_001080122.3:c.180_227del
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2019-03-27
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001064781
ClinVar Disease
Huntington disease-like 1
Observed Origin Sample
germline
Drugs