Annotation Detail

Information
Associated Genes
STK11
Associated Variants
STK11 p.Ser240Trp (p.S240W) ( ENST00000326873.12, ENST00000585465.3, ENST00000652231.1, ENST00000714322.1, ENST00000714323.1 )
STK11 p.Ser240Trp (p.S240W) ( ENST00000326873.12, ENST00000585465.3, ENST00000652231.1, ENST00000714322.1, ENST00000714323.1 )
Associated Disease
Peutz-Jeghers syndrome
Source Database
ClinVar
Description
NM_000455.5(STK11):c.719C>G (p.Ser240Trp) AND Peutz-Jeghers syndrome
ClinVar Allele ID
181068
ClinVar RefSeq Alternation Syntax
NM_000455.5:c.719C>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2023-03-23
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001041130
ClinVar Disease
Peutz-Jeghers syndrome
Observed Origin Sample
germline
Drugs