Annotation Detail

Information
Associated Genes
ERCC4
Associated Variants
ERCC4 p.Arg799Trp (p.R799W) ( ENST00000311895.8, ENST00000682617.1 )
ERCC4 p.Arg799Trp (p.R799W) ( ENST00000311895.8, ENST00000682617.1 )
Associated Disease
Hutchinson-Gilford syndrome
Source Database
ClinVar
Description
NM_005236.3(ERCC4):c.2395C>T (p.Arg799Trp) AND Hutchinson-Gilford syndrome
ClinVar Allele ID
31619
ClinVar RefSeq Alternation Syntax
NM_005236.3:c.2395C>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001034542
ClinVar Disease
Hutchinson-Gilford syndrome
Observed Origin Sample
unknown
Drugs