Annotation Detail

Information
Associated Genes
POLG POLGARF
Associated Variants
POLG p.Thr251Ile (p.T251I) ( ENST00000636937.2, ENST00000268124.11, ENST00000442287.6 )
POLG p.Thr251Ile (p.T251I) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Progressive sclerosing poliodystrophy mitochondrial DNA depletion syndrome 4b
Source Database
ClinVar
Description
NM_002693.3(POLG):c.752C>T (p.Thr251Ile) AND multiple conditions
ClinVar Allele ID
28542
ClinVar RefSeq Alternation Syntax
NM_001126131.2:c.752C>T
ClinVar RefSeq Alternation Syntax
NM_002693.3:c.752C>T
Clinical Significance Description
Pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001004407
ClinVar Disease
Progressive sclerosing poliodystrophy
ClinVar Disease
Mitochondrial DNA depletion syndrome 4b
Observed Origin Sample
germline
Drugs