Annotation Detail

Information
Associated Genes
TMEM231
Associated Variants
TMEM231 p.Leu81Phe (p.L81F) ( ENST00000568377.5, ENST00000685935.1, ENST00000693682.1, ENST00000565067.5, ENST00000258173.11 )
TMEM231 p.Leu81Phe (p.L81F) ( ENST00000258173.11, ENST00000565067.5, ENST00000568377.5, ENST00000685935.1, ENST00000693682.1 )
Associated Disease
ciliopathy
Source Database
ClinVar
Description
NM_001077418.3(TMEM231):c.241C>T (p.Leu81Phe) AND Ciliopathy
ClinVar Allele ID
439090
ClinVar RefSeq Alternation Syntax
NR_074083.2:n.284C>T
ClinVar RefSeq Alternation Syntax
NM_001077416.2:c.400C>T
ClinVar RefSeq Alternation Syntax
NM_001077418.3:c.241C>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2019-06-23
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001003228
ClinVar Disease
Ciliopathy
Observed Origin Sample
inherited
Drugs