Annotation Detail

Information
Associated Genes
COL2A1
Associated Variants
COL2A1 p.Arg1036Ter (p.R1036*) ( ENST00000380518.8, ENST00000337299.7 )
COL2A1 p.Arg1036Ter (p.R1036*) ( ENST00000337299.7, ENST00000380518.8 )
Associated Disease
Stickler syndrome type 1
Source Database
ClinVar
Description
NM_001844.5(COL2A1):c.3106C>T (p.Arg1036Ter) AND Stickler syndrome type 1
ClinVar Allele ID
194664
ClinVar RefSeq Alternation Syntax
NM_033150.3:c.2899C>T
ClinVar RefSeq Alternation Syntax
NM_001844.5:c.3106C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-05-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000988819
ClinVar Disease
Stickler syndrome type 1
Observed Origin Sample
unknown
Drugs