Annotation Detail

Information
Associated Genes
HBB LOC107133510 LOC110006319
Associated Variants
HBB p.Glu122Ter (p.E122*) ( ENST00000335295.4, ENST00000647020.1 )
HBB p.Glu122Ter (p.E122*) ( ENST00000335295.4, ENST00000647020.1 )
Associated Disease
beta thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.364G>T (p.Glu122Ter) AND beta Thalassemia
ClinVar Allele ID
30443
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.364G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-01-22
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000984185
ClinVar Disease
beta Thalassemia
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs