Annotation Detail

Information
Associated Genes
PEX10
Associated Variants
PEX10 c.836+9G>A ( ENST00000507596.5, ENST00000447513.7, ENST00000288774.8 )
PEX10 c.836+9G>A ( ENST00000288774.8, ENST00000447513.7, ENST00000507596.5 )
Associated Disease
Peroxisome biogenesis disorder, complementation group 7
Source Database
ClinVar
Description
NM_002617.4(PEX10):c.776+9G>A AND Peroxisome biogenesis disorder, complementation group 7
ClinVar Allele ID
774478
ClinVar RefSeq Alternation Syntax
NM_001374427.1:c.344+9G>A
ClinVar RefSeq Alternation Syntax
NM_153818.2:c.836+9G>A
ClinVar RefSeq Alternation Syntax
NM_002617.4:c.776+9G>A
ClinVar RefSeq Alternation Syntax
NM_001374426.1:c.401+9G>A
ClinVar RefSeq Alternation Syntax
NM_001374425.1:c.833+9G>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2024-01-30
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000941540
ClinVar Disease
Peroxisome biogenesis disorder, complementation group 7
Observed Origin Sample
germline
Drugs