Annotation Detail

Information
Associated Genes
TTR
Associated Variants
TTR p.Val142Ile (p.V142I) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
TTR p.Val142Ile (p.V142I) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
Associated Disease
ATTRV122I amyloidosis
Source Database
ClinVar
Description
NM_000371.4(TTR):c.424G>A (p.Val142Ile) AND ATTRV122I amyloidosis
ClinVar Allele ID
28465
ClinVar RefSeq Alternation Syntax
NM_000371.4:c.424G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-03-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000853387
ClinVar Disease
ATTRV122I amyloidosis
Observed Origin Sample
germline
Drugs