Annotation Detail

Information
Associated Genes
KRAS
Associated Variants
KRAS p.Pro34Arg (p.P34R) ( ENST00000256078.10, ENST00000311936.8, ENST00000556131.2, ENST00000557334.6, ENST00000685328.1, ENST00000686969.1, ENST00000688940.1, ENST00000692768.1, ENST00000693229.1 )
KRAS p.Pro34Arg (p.P34R) ( ENST00000256078.10, ENST00000311936.8, ENST00000556131.2, ENST00000557334.6, ENST00000685328.1, ENST00000686969.1, ENST00000688940.1, ENST00000692768.1, ENST00000693229.1 )
Associated Disease
cardiofaciocutaneous syndrome 2 Noonan syndrome 3 autoimmune lymphoproliferative syndrome type 4 acute myeloid leukemia
Source Database
ClinVar
Description
NM_004985.5(KRAS):c.101C>G (p.Pro34Arg) AND multiple conditions
ClinVar Allele ID
27629
ClinVar RefSeq Alternation Syntax
NM_004985.5:c.101C>G
ClinVar RefSeq Alternation Syntax
NM_033360.4:c.101C>G
ClinVar RefSeq Alternation Syntax
NM_001369786.1:c.101C>G
ClinVar RefSeq Alternation Syntax
NM_001369787.1:c.101C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-12-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000850569
ClinVar Disease
Cardiofaciocutaneous syndrome 2
ClinVar Disease
Noonan syndrome 3
ClinVar Disease
Autoimmune lymphoproliferative syndrome type 4
ClinVar Disease
Acute myeloid leukemia
Observed Origin Sample
germline
Drugs