Annotation Detail

Information
Associated Genes
COL7A1
Associated Variants
COL7A1 p.Gly2031Ser (p.G2031S) ( ENST00000328333.12, ENST00000681320.1 )
COL7A1 p.Gly2031Ser (p.G2031S) ( ENST00000328333.12, ENST00000681320.1 )
Associated Disease
pretibial dystrophic epidermolysis bullosa Epidermolysis bullosa pruriginosa transient bullous dermolysis of the newborn Dominant dystrophic epidermolysis bullosa with absence of skin nonsyndromic congenital nail disorder 8 Generalized dominant dystrophic epidermolysis bullosa recessive dystrophic epidermolysis bullosa
Source Database
ClinVar
Description
NM_000094.4(COL7A1):c.6091G>A (p.Gly2031Ser) AND multiple conditions
ClinVar Allele ID
32485
ClinVar RefSeq Alternation Syntax
NM_000094.4:c.6091G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2012-09-20
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000850543
ClinVar Disease
Transient bullous dermolysis of the newborn
ClinVar Disease
Recessive dystrophic epidermolysis bullosa
ClinVar Disease
Dominant dystrophic epidermolysis bullosa with absence of skin
ClinVar Disease
Nonsyndromic congenital nail disorder 8
ClinVar Disease
Epidermolysis bullosa pruriginosa
ClinVar Disease
Pretibial dystrophic epidermolysis bullosa
ClinVar Disease
Generalized dominant dystrophic epidermolysis bullosa
Observed Origin Sample
germline
Drugs