Annotation Detail

Information
Associated Genes
PRX
Associated Variants
PRX p.Ala795ProfsTer18 (p.A795Pfs*18) ( ENST00000291825.11, ENST00000324001.8, ENST00000673881.1, ENST00000674005.2, ENST00000674773.1 )
PRX p.Ala795ProfsTer18 (p.A795Pfs*18) ( ENST00000291825.11, ENST00000324001.8, ENST00000673881.1, ENST00000674005.2, ENST00000674773.1 )
Associated Disease
Charcot-Marie-Tooth disease
Source Database
ClinVar
Description
NM_181882.3(PRX):c.2098del (p.Ala700fs) AND Charcot-Marie-Tooth disease
ClinVar Allele ID
47012
ClinVar RefSeq Alternation Syntax
NM_181882.3:c.2098del
ClinVar RefSeq Alternation Syntax
NM_020956.2:c.*2303del
Clinical Significance Description
Uncertain significance
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000790179
ClinVar Disease
Charcot-Marie-Tooth disease
Observed Origin Sample
germline
Drugs