Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 p.Arg2030Gln (p.R2030Q) ( ENST00000370225.4 )
ABCA4 p.Arg2030Gln (p.R2030Q) ( ENST00000370225.4 )
Associated Disease
Progressive cone dystrophy (without rod involvement)
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.6089G>A (p.Arg2030Gln) AND Progressive cone dystrophy (without rod involvement)
ClinVar Allele ID
105317
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.6089G>A
ClinVar RefSeq Alternation Syntax
NM_001425324.1:c.5867G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000787766
ClinVar Disease
Progressive cone dystrophy (without rod involvement)
Observed Origin Sample
unknown
Drugs