Annotation Detail

Information
Associated Genes
CCNH RASA1
Associated Variants
RASA1 p.Arg711Ter (p.R711*) ( ENST00000274376.11, ENST00000456692.6, ENST00000506290.1, ENST00000512763.5 )
RASA1 p.Arg711Ter (p.R711*) ( ENST00000274376.11, ENST00000456692.6, ENST00000506290.1, ENST00000512763.5 )
Associated Disease
Capillary malformation-arteriovenous malformation 1 Basal cell carcinoma, susceptibility to, 1
Source Database
ClinVar
Description
NM_002890.3(RASA1):c.2131C>T (p.Arg711Ter) AND multiple conditions
ClinVar Allele ID
209861
ClinVar RefSeq Alternation Syntax
NM_002890.3:c.2131C>T
ClinVar RefSeq Alternation Syntax
NM_001364075.2:c.933+18532G>A
ClinVar RefSeq Alternation Syntax
NM_022650.3:c.1600C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-01-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000763548
ClinVar Disease
Basal cell carcinoma, susceptibility to, 1
ClinVar Disease
Capillary malformation-arteriovenous malformation 1
Observed Origin Sample
unknown
Drugs