Annotation Detail

Information
Associated Genes
TTR
Associated Variants
TTR p.Phe84Leu (p.F84L) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
TTR p.Phe84Leu (p.F84L) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
Associated Disease
Hyperthyroxinemia, dystransthyretinemic carpal tunnel syndrome Familial amyloid neuropathy
Source Database
ClinVar
Description
NM_000371.4(TTR):c.250T>C (p.Phe84Leu) AND multiple conditions
ClinVar Allele ID
28492
ClinVar RefSeq Alternation Syntax
NM_000371.4:c.250T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2018-10-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000763027
ClinVar Disease
Carpal tunnel syndrome
ClinVar Disease
Hyperthyroxinemia, dystransthyretinemic
ClinVar Disease
Familial amyloid neuropathy
Observed Origin Sample
unknown
Drugs