Annotation Detail

Information
Associated Genes
SLC2A1
Associated Variants
SLC2A1 p.Arg458Trp (p.R458W) ( ENST00000426263.10, ENST00000674765.1 )
SLC2A1 p.Arg458Trp (p.R458W) ( ENST00000426263.10, ENST00000674765.1 )
Associated Disease
Encephalopathy due to GLUT1 deficiency dystonia 9 Childhood onset GLUT1 deficiency syndrome 2 Epilepsy, idiopathic generalized, susceptibility to, 12 Hereditary cryohydrocytosis with reduced stomatin
Source Database
ClinVar
Description
NM_006516.4(SLC2A1):c.1372C>T (p.Arg458Trp) AND multiple conditions
ClinVar Allele ID
102597
ClinVar RefSeq Alternation Syntax
NM_006516.4:c.1372C>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2018-10-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000762930
ClinVar Disease
Epilepsy, idiopathic generalized, susceptibility to, 12
ClinVar Disease
Encephalopathy due to GLUT1 deficiency
ClinVar Disease
Hereditary cryohydrocytosis with reduced stomatin
ClinVar Disease
Dystonia 9
ClinVar Disease
Childhood onset GLUT1 deficiency syndrome 2
Observed Origin Sample
unknown
Drugs