Annotation Detail

Information
Associated Genes
MRE11
Associated Variants
MRE11 p.Met26Thr (p.M26T) ( ENST00000323929.8, ENST00000323977.7, ENST00000393241.8, ENST00000407439.7, ENST00000540013.5 )
MRE11 p.Met26Thr (p.M26T) ( ENST00000323929.8, ENST00000323977.7, ENST00000393241.8, ENST00000407439.7, ENST00000540013.5 )
Associated Disease
Ataxia-telangiectasia-like disorder 1
Source Database
ClinVar
Description
NM_005591.4(MRE11):c.77T>C (p.Met26Thr) AND Ataxia-telangiectasia-like disorder 1
ClinVar Allele ID
180546
ClinVar RefSeq Alternation Syntax
NM_005590.4:c.77T>C
ClinVar RefSeq Alternation Syntax
NM_001330347.2:c.77T>C
ClinVar RefSeq Alternation Syntax
NM_005591.4:c.77T>C
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2023-10-20
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000684815
ClinVar Disease
Ataxia-telangiectasia-like disorder 1
Observed Origin Sample
germline
Observed Origin Sample
maternal
Observed Origin Sample
unknown
Drugs