Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Arg184Gln (p.R184Q) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Arg184Gln (p.R184Q) ( ENST00000382844.2, ENST00000382848.5 )
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.551G>A (p.Arg184Gln) AND Hearing loss
ClinVar Allele ID
38617
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.551G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-04-07
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000678889
Observed Origin Sample
germline
Drugs