Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Arg143Trp (p.R143W) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Arg143Trp (p.R143W) ( ENST00000382844.2, ENST00000382848.5 )
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.427C>T (p.Arg143Trp) AND Hearing loss
ClinVar Allele ID
32048
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.427C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-10-02
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000678885
Observed Origin Sample
germline
Drugs