Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.His100Tyr (p.H100Y) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.His100Tyr (p.H100Y) ( ENST00000382844.2, ENST00000382848.5 )
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.298C>T (p.His100Tyr) AND Hearing loss
ClinVar Allele ID
169011
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.298C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2003-02-14
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000678877
Observed Origin Sample
germline
Drugs