Annotation Detail

Information
Associated Genes
C8B
Associated Variants
C8B p.Trp551Ter (p.W551*) ( ENST00000371237.9, ENST00000696164.1, ENST00000695842.1 )
C8B p.Trp551Ter (p.W551*) ( ENST00000371237.9, ENST00000695842.1, ENST00000696164.1 )
Associated Disease
type II complement component 8 deficiency
Source Database
ClinVar
Description
NM_000066.4(C8B):c.1653G>A (p.Trp551Ter) AND Type II complement component 8 deficiency
ClinVar Allele ID
550315
ClinVar RefSeq Alternation Syntax
NM_000066.4:c.1653G>A
ClinVar RefSeq Alternation Syntax
NM_001278544.2:c.1467G>A
ClinVar RefSeq Alternation Syntax
NM_001278543.2:c.1497G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000677371
ClinVar Disease
Type II complement component 8 deficiency
Observed Origin Sample
germline
Drugs