Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Gly12Asp (p.G12D) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Gly12Asp (p.G12D) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
Autosomal recessive nonsyndromic hearing loss 1A
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.35G>A (p.Gly12Asp) AND Autosomal recessive nonsyndromic hearing loss 1A
ClinVar Allele ID
547105
ClinVar RefSeq Alternation Syntax
NM_004004.6:c.35G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2017-04-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000666230
ClinVar Disease
Autosomal recessive nonsyndromic hearing loss 1A
Observed Origin Sample
unknown
Drugs