Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB c.92+2T>A ( ENST00000647020.1, ENST00000485743.1, ENST00000335295.4 )
HBB c.92+2T>A ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
beta thalassemia
Source Database
ClinVar
Description
NM_000518.5(HBB):c.92+2T>A AND beta Thalassemia
ClinVar Allele ID
47272
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.92+2T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2019-05-06
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000665219
ClinVar Disease
beta Thalassemia
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs