Annotation Detail

Information
Associated Genes
SDHA
Associated Variants
ENSG00000286001 p.? (p.?), SDHA p.? (p.?) ( ENST00000510361.5, ENST00000504309.5, ENST00000264932.11 )
ENSG00000286001 p.? (p.?), SDHA p.? (p.?) ( ENST00000264932.11, ENST00000504309.5, ENST00000510361.5 )
Associated Disease
Paragangliomas 5
Source Database
ClinVar
Description
NM_004168.4(SDHA):c.2T>C (p.Met1Thr) AND Paragangliomas 5
ClinVar Allele ID
394857
ClinVar RefSeq Alternation Syntax
NM_001330758.2:c.2T>C
ClinVar RefSeq Alternation Syntax
NM_004168.4:c.2T>C
ClinVar RefSeq Alternation Syntax
NM_001294332.2:c.2T>C
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2023-04-24
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000662887
ClinVar Disease
Paragangliomas 5
Observed Origin Sample
unknown
Drugs