Annotation Detail

Information
Associated Genes
KIT
Associated Variants
KIT p.Asp817Val (p.D817V) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687109.1, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
KIT p.Asp817Val (p.D817V) ( ENST00000686011.1, ENST00000687109.1, ENST00000288135.6, ENST00000412167.7, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
Associated Disease
MASTOCYTOSIS WITH ASSOCIATED HEMATOLOGIC DISORDER, SOMATIC
Source Database
ClinVar
Description
NM_000222.3(KIT):c.2447A>T (p.Asp816Val) AND MASTOCYTOSIS WITH ASSOCIATED HEMATOLOGIC DISORDER, SOMATIC
ClinVar Allele ID
28891
ClinVar RefSeq Alternation Syntax
NM_001385284.1:c.2450A>T
ClinVar RefSeq Alternation Syntax
NM_001385290.1:c.2447A>T
ClinVar RefSeq Alternation Syntax
NM_001385286.1:c.2432A>T
ClinVar RefSeq Alternation Syntax
NM_001385292.1:c.2435A>T
ClinVar RefSeq Alternation Syntax
NM_001385288.1:c.2438A>T
ClinVar RefSeq Alternation Syntax
NM_001093772.2:c.2435A>T
ClinVar RefSeq Alternation Syntax
NM_000222.3:c.2447A>T
ClinVar RefSeq Alternation Syntax
NM_001385285.1:c.2444A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2001-08-15
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000656674
ClinVar Disease
MASTOCYTOSIS WITH ASSOCIATED HEMATOLOGIC DISORDER, SOMATIC
Observed Origin Sample
somatic
Pubmed
19262599
Pubmed
7479840
Pubmed
9990072
Pubmed
9827716
Pubmed
11380399
Pubmed
8589724
Pubmed
7691885
Pubmed
11493470
Pubmed
19865100
Drugs