Annotation Detail

Information
Associated Genes
DICER1
Associated Variants
DICER1 c.*88T>A ( ENST00000393063.6, ENST00000529720.2, ENST00000343455.8, ENST00000527414.5, ENST00000674628.2, ENST00000531162.7, ENST00000526495.6 )
DICER1 c.*88T>A ( ENST00000343455.8, ENST00000393063.6, ENST00000526495.6, ENST00000527414.5, ENST00000529720.2, ENST00000531162.7, ENST00000674628.2 )
Associated Disease
DICER1-related tumor predisposition
Source Database
ClinVar
Description
NM_177438.3(DICER1):c.*88T>A AND DICER1-related tumor predisposition
ClinVar Allele ID
321919
ClinVar RefSeq Alternation Syntax
NM_001195573.1:c.*204T>A
ClinVar RefSeq Alternation Syntax
NM_001271282.3:c.*88T>A
ClinVar RefSeq Alternation Syntax
NM_030621.4:c.*88T>A
ClinVar RefSeq Alternation Syntax
NM_001291628.2:c.*88T>A
ClinVar RefSeq Alternation Syntax
NM_177438.3:c.*88T>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2024-01-29
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000654483
ClinVar Disease
DICER1-related tumor predisposition
Observed Origin Sample
germline
Drugs