Annotation Detail

Information
Associated Genes
TIA1
Associated Variants
TIA1 p.Asp104Val (p.D104V) ( ENST00000282574.8, ENST00000415783.6, ENST00000416149.6, ENST00000433529.7, ENST00000445587.5 )
TIA1 p.Asp104Val (p.D104V) ( ENST00000282574.8, ENST00000415783.6, ENST00000416149.6, ENST00000433529.7, ENST00000445587.5 )
Associated Disease
Welander distal myopathy
Source Database
ClinVar
Description
NM_022173.4(TIA1):c.311A>T (p.Asp104Val) AND Welander distal myopathy
ClinVar Allele ID
518512
ClinVar RefSeq Alternation Syntax
NM_001351508.2:c.311A>T
ClinVar RefSeq Alternation Syntax
NR_147226.2:n.476A>T
ClinVar RefSeq Alternation Syntax
NR_147230.2:n.628A>T
ClinVar RefSeq Alternation Syntax
NR_147231.2:n.509A>T
ClinVar RefSeq Alternation Syntax
NR_147228.2:n.509A>T
ClinVar RefSeq Alternation Syntax
NR_147232.2:n.379A>T
ClinVar RefSeq Alternation Syntax
NR_147229.2:n.476A>T
ClinVar RefSeq Alternation Syntax
NM_001351523.2:c.83A>T
ClinVar RefSeq Alternation Syntax
NM_001351509.2:c.284A>T
ClinVar RefSeq Alternation Syntax
NM_001351518.2:c.311A>T
ClinVar RefSeq Alternation Syntax
NM_001351510.2:c.278A>T
ClinVar RefSeq Alternation Syntax
NR_147222.2:n.471A>T
ClinVar RefSeq Alternation Syntax
NR_147223.2:n.595A>T
ClinVar RefSeq Alternation Syntax
NM_001351524.2:c.-110A>T
ClinVar RefSeq Alternation Syntax
NM_001351519.2:c.311A>T
ClinVar RefSeq Alternation Syntax
NM_001351515.2:c.8A>T
ClinVar RefSeq Alternation Syntax
NM_001351520.2:c.436A>T
ClinVar RefSeq Alternation Syntax
NR_147224.2:n.476A>T
ClinVar RefSeq Alternation Syntax
NM_001351525.2:c.-176A>T
ClinVar RefSeq Alternation Syntax
NR_147221.2:n.476A>T
ClinVar RefSeq Alternation Syntax
NM_001351513.1:c.167A>T
ClinVar RefSeq Alternation Syntax
NR_147218.1:n.416A>T
ClinVar RefSeq Alternation Syntax
NM_001351522.2:c.311A>T
ClinVar RefSeq Alternation Syntax
NR_147219.2:n.509A>T
ClinVar RefSeq Alternation Syntax
NM_001351516.2:c.311A>T
ClinVar RefSeq Alternation Syntax
NM_022173.4:c.311A>T
ClinVar RefSeq Alternation Syntax
NM_001351511.1:c.200A>T
ClinVar RefSeq Alternation Syntax
NR_147216.1:n.535A>T
ClinVar RefSeq Alternation Syntax
NM_001351512.1:c.173A>T
ClinVar RefSeq Alternation Syntax
NM_022037.4:c.278A>T
ClinVar RefSeq Alternation Syntax
NR_147227.2:n.504A>T
ClinVar RefSeq Alternation Syntax
NM_001351514.2:c.83A>T
ClinVar RefSeq Alternation Syntax
NM_001351517.2:c.-214A>T
ClinVar RefSeq Alternation Syntax
NR_147220.2:n.471A>T
ClinVar RefSeq Alternation Syntax
NR_147225.2:n.628A>T
ClinVar RefSeq Alternation Syntax
NM_001351521.2:c.278A>T
ClinVar RefSeq Alternation Syntax
NR_147217.1:n.416A>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2019-06-26
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000633709
ClinVar Disease
Welander distal myopathy
Observed Origin Sample
germline
Drugs