Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Arg192Ter (p.R192*) ( ENST00000490416.2, ENST00000487476.5, ENST00000356175.7, ENST00000358273.9, ENST00000431387.8, ENST00000691014.1, ENST00000696138.1 )
NF1 p.Arg192Ter (p.R192*) ( ENST00000356175.7, ENST00000358273.9, ENST00000431387.8, ENST00000487476.5, ENST00000490416.2, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
Cafe au lait spots, multiple
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.574C>T (p.Arg192Ter) AND multiple conditions
ClinVar Allele ID
48599
ClinVar RefSeq Alternation Syntax
NM_001128147.3:c.574C>T
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.574C>T
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.574C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-01-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000626737
ClinVar Disease
Cafe au lait spots, multiple
Observed Origin Sample
unknown
Drugs