Annotation Detail

Information
Associated Genes
MEFV
Associated Variants
MEFV p.Val726Ala (p.V726A) ( ENST00000536379.5, ENST00000541159.5, ENST00000219596.6, ENST00000339854.8 )
MEFV p.Val726Ala (p.V726A) ( ENST00000219596.6, ENST00000339854.8, ENST00000536379.5, ENST00000541159.5 )
Associated Disease
Inborn genetic diseases
Source Database
ClinVar
Description
NM_000243.3(MEFV):c.2177T>C (p.Val726Ala) AND Inborn genetic diseases
ClinVar Allele ID
17579
ClinVar RefSeq Alternation Syntax
NM_001198536.2:c.*381T>C
ClinVar RefSeq Alternation Syntax
NM_000243.3:c.2177T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000623003
ClinVar Disease
Inborn genetic diseases
Observed Origin Sample
germline
Drugs