Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Val141Met (p.V141M) ( ENST00000496887.7, ENST00000335475.6, ENST00000155840.12, ENST00000646564.2, ENST00000713725.1 )
KCNQ1 p.Val141Met (p.V141M) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
Source Database
ClinVar
Description
NM_000218.3(KCNQ1):c.421G>A (p.Val141Met) AND Cardiovascular phenotype
ClinVar Allele ID
77968
ClinVar RefSeq Alternation Syntax
NM_000218.3:c.421G>A
ClinVar RefSeq Alternation Syntax
NM_181798.2:c.40G>A
ClinVar RefSeq Alternation Syntax
NM_001406838.1:c.421G>A
ClinVar RefSeq Alternation Syntax
NM_001406837.1:c.151G>A
ClinVar RefSeq Alternation Syntax
NM_001406836.1:c.421G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2016-12-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000621525
Observed Origin Sample
germline
Drugs