Annotation Detail

Information
Associated Genes
PAPSS2
Associated Variants
PAPSS2 p.Tyr74Ter (p.Y74*) ( ENST00000456849.2, ENST00000361175.8 )
PAPSS2 p.Tyr74Ter (p.Y74*) ( ENST00000361175.8, ENST00000456849.2 )
Associated Disease
brachyolmia
Source Database
ClinVar
Description
NM_001015880.2(PAPSS2):c.222C>G (p.Tyr74Ter) AND Brachyolmia
ClinVar Allele ID
496550
ClinVar RefSeq Alternation Syntax
NM_001015880.2:c.222C>G
ClinVar RefSeq Alternation Syntax
NM_004670.4:c.222C>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2017-04-28
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000611427
ClinVar Disease
Brachyolmia
Observed Origin Sample
germline
Drugs