Annotation Detail

Information
Associated Genes
LDLR
Associated Variants
LDLR p.Cys27Trp (p.C27W) ( ENST00000252444.10, ENST00000455727.6, ENST00000535915.5, ENST00000545707.5, ENST00000557933.5, ENST00000558013.5, ENST00000558518.6, ENST00000560467.2 )
LDLR p.Cys27Trp (p.C27W) ( ENST00000252444.10, ENST00000455727.6, ENST00000535915.5, ENST00000545707.5, ENST00000557933.5, ENST00000558013.5, ENST00000558518.6, ENST00000560467.2 )
Associated Disease
familial hypercholesterolemia
Source Database
ClinVar
Description
NM_000527.5(LDLR):c.81C>G (p.Cys27Trp) AND Familial hypercholesterolemia
ClinVar Allele ID
228117
ClinVar RefSeq Alternation Syntax
NM_001195803.2:c.81C>G
ClinVar RefSeq Alternation Syntax
NM_001195799.2:c.81C>G
ClinVar RefSeq Alternation Syntax
NM_001195798.2:c.81C>G
ClinVar RefSeq Alternation Syntax
NM_001195800.2:c.81C>G
ClinVar RefSeq Alternation Syntax
NM_000527.5:c.81C>G
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2024-01-29
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000588365
ClinVar Disease
Familial hypercholesterolemia
Observed Origin Sample
germline
Drugs