Annotation Detail

Information
Associated Genes
VHL LOC107303340
Associated Variants
VHL p.Arg161Gln (p.R161Q) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
VHL p.Arg161Gln (p.R161Q) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000551.4(VHL):c.482G>A (p.Arg161Gln) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
180121
ClinVar RefSeq Alternation Syntax
NM_001354723.2:c.*36G>A
ClinVar RefSeq Alternation Syntax
NM_198156.3:c.359G>A
ClinVar RefSeq Alternation Syntax
NM_000551.4:c.482G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-12-07
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000563066
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs