Annotation Detail

Information
Associated Genes
ATP1A3
Associated Variants
ATP1A3 p.Ser824Pro (p.S824P), ENSG00000285505 p.Ser811Pro (p.S811P) ( ENST00000543770.5, ENST00000545399.6, ENST00000602133.5, ENST00000648268.1 )
ATP1A3 p.Ser824Pro (p.S824P), ENSG00000285505 p.Ser811Pro (p.S811P) ( ENST00000543770.5, ENST00000545399.6, ENST00000602133.5, ENST00000648268.1 )
Associated Disease
dystonia 12
Source Database
ClinVar
Description
NM_152296.5(ATP1A3):c.2431T>C (p.Ser811Pro) AND Dystonia 12
ClinVar Allele ID
45779
ClinVar RefSeq Alternation Syntax
NM_001256213.2:c.2464T>C
ClinVar RefSeq Alternation Syntax
NM_001256214.2:c.2470T>C
ClinVar RefSeq Alternation Syntax
NM_152296.5:c.2431T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000541711
ClinVar Disease
Dystonia 12
Observed Origin Sample
germline
Drugs