Annotation Detail

Information
Associated Genes
GLI3
Associated Variants
GLI3 p.Asn503= (p.N503=) ( ENST00000479210.1, ENST00000395925.8, ENST00000677288.1, ENST00000677605.1 )
GLI3 p.Asn503= (p.N503=) ( ENST00000677288.1, ENST00000395925.8, ENST00000479210.1, ENST00000677605.1 )
Associated Disease
Pallister-Hall syndrome Greig cephalopolysyndactyly syndrome
Source Database
ClinVar
Description
NM_000168.6(GLI3):c.1509C>T (p.Asn503=) AND multiple conditions
ClinVar Allele ID
252864
ClinVar RefSeq Alternation Syntax
NM_000168.6:c.1509C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2024-01-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000528681
ClinVar Disease
Greig cephalopolysyndactyly syndrome
ClinVar Disease
Pallister-Hall syndrome
Observed Origin Sample
germline
Drugs