Annotation Detail

Information
Associated Genes
POLG POLGARF
Associated Variants
POLG p.Gly737Arg (p.G737R) ( ENST00000442287.6, ENST00000268124.11, ENST00000636937.2 )
POLG p.Gly737Arg (p.G737R) ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2 )
Associated Disease
Mitochondrial disease
Source Database
ClinVar
Description
NM_002693.3(POLG):c.2209G>C (p.Gly737Arg) AND Mitochondrial disease
ClinVar Allele ID
28552
ClinVar RefSeq Alternation Syntax
NM_001126131.2:c.2209G>C
ClinVar RefSeq Alternation Syntax
NM_002693.3:c.2209G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-04-07
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000508744
ClinVar Disease
Mitochondrial disease
Observed Origin Sample
germline
Drugs