Annotation Detail

Information
Associated Genes
MAOA
Associated Variants
MAOA p.Val244Ile (p.V244I) ( ENST00000338702.4, ENST00000542639.6, ENST00000686683.1, ENST00000688006.1, ENST00000689087.1, ENST00000693128.1 )
MAOA p.Val244Ile (p.V244I) ( ENST00000338702.4, ENST00000542639.6, ENST00000686683.1, ENST00000688006.1, ENST00000689087.1, ENST00000693128.1 )
Associated Disease
Brunner Syndrome
Source Database
ClinVar
Description
NM_000240.4(MAOA):c.730G>A (p.Val244Ile) AND Brunner syndrome
ClinVar Allele ID
424619
ClinVar RefSeq Alternation Syntax
NM_000240.4:c.730G>A
ClinVar RefSeq Alternation Syntax
NM_001270458.2:c.331G>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2017-08-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000496099
ClinVar Disease
Brunner syndrome
Observed Origin Sample
maternal
Drugs