Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Leu79CysfsTer3 (p.L79Cfs*3) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Leu79CysfsTer3 (p.L79Cfs*3) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
Autosomal recessive nonsyndromic hearing loss 1A Autosomal dominant nonsyndromic hearing loss 3A
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.235del (p.Leu79fs) AND multiple conditions
ClinVar Allele ID
32053
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2016-03-18
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000490501
ClinVar Disease
Autosomal recessive nonsyndromic hearing loss 1A
ClinVar Disease
Autosomal dominant nonsyndromic hearing loss 3A
Observed Origin Sample
germline
Drugs