Annotation Detail

Information
Associated Genes
STK11
Associated Variants
STK11 p.Asp176Asn (p.D176N) ( ENST00000585465.3, ENST00000326873.12, ENST00000652231.1, ENST00000714322.1, ENST00000714323.1 )
STK11 p.Asp176Asn (p.D176N) ( ENST00000326873.12, ENST00000585465.3, ENST00000652231.1, ENST00000714322.1, ENST00000714323.1 )
Associated Disease
Peutz-Jeghers syndrome
Source Database
ClinVar
Description
NM_000455.5(STK11):c.526G>A (p.Asp176Asn) AND Peutz-Jeghers syndrome
ClinVar Allele ID
181057
ClinVar RefSeq Alternation Syntax
NM_000455.5:c.526G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-09-09
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000429467
ClinVar Disease
Peutz-Jeghers syndrome
Observed Origin Sample
germline
Observed Origin Sample
somatic
Drugs