Annotation Detail

Information
Associated Genes
PAH
Associated Variants
PAH p.Pro211Thr (p.P211T) ( ENST00000553106.6, ENST00000307000.7 )
PAH p.Pro211Thr (p.P211T) ( ENST00000307000.7, ENST00000553106.6 )
Associated Disease
phenylketonuria
Source Database
ClinVar
Description
NM_000277.3(PAH):c.631C>A (p.Pro211Thr) AND Phenylketonuria
ClinVar Allele ID
108502
ClinVar RefSeq Alternation Syntax
NM_000277.3:c.631C>A
ClinVar RefSeq Alternation Syntax
NM_001354304.2:c.631C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-07-03
Clinical Significance Review Status
reviewed by expert panel
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000411219
ClinVar Disease
Phenylketonuria
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs