Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Pro354Gln (p.P354Q) ( ENST00000700029.2, ENST00000371953.8, ENST00000688308.1, ENST00000700021.1, ENST00000713839.1 )
PTEN p.Pro354Gln (p.P354Q) ( ENST00000371953.8, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
Cowden syndrome 1
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.1061C>A (p.Pro354Gln) AND Cowden syndrome 1
ClinVar Allele ID
152734
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.1580C>A
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.1061C>A
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.470C>A
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2023-04-05
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000409006
ClinVar Disease
Cowden syndrome 1
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs