Annotation Detail

Information
Associated Genes
MTRR
Associated Variants
MTRR c.*541G>A ( ENST00000264668.6, ENST00000440940.7 )
MTRR c.*541G>A ( ENST00000264668.6, ENST00000440940.7 )
Associated Disease
Disorders of Intracellular Cobalamin Metabolism
Source Database
ClinVar
Description
NM_002454.3(MTRR):c.*541G>A AND Disorders of Intracellular Cobalamin Metabolism
ClinVar Allele ID
298206
ClinVar RefSeq Alternation Syntax
NM_001364441.2:c.*541G>A
ClinVar RefSeq Alternation Syntax
NR_157173.2:n.2728G>A
ClinVar RefSeq Alternation Syntax
NR_157169.2:n.2551G>A
ClinVar RefSeq Alternation Syntax
NM_001364442.2:c.*541G>A
ClinVar RefSeq Alternation Syntax
NR_157175.2:n.2883G>A
ClinVar RefSeq Alternation Syntax
NM_002454.3:c.*541G>A
ClinVar RefSeq Alternation Syntax
NR_157168.2:n.2691G>A
ClinVar RefSeq Alternation Syntax
NR_134481.2:n.2642G>A
ClinVar RefSeq Alternation Syntax
NR_157177.2:n.2726G>A
ClinVar RefSeq Alternation Syntax
NM_024010.4:c.*541G>A
ClinVar RefSeq Alternation Syntax
NR_134480.2:n.2717G>A
ClinVar RefSeq Alternation Syntax
NR_157171.2:n.2574G>A
ClinVar RefSeq Alternation Syntax
NR_134482.2:n.2577G>A
ClinVar RefSeq Alternation Syntax
NR_157172.2:n.2488G>A
ClinVar RefSeq Alternation Syntax
NR_157176.2:n.3046G>A
ClinVar RefSeq Alternation Syntax
NR_157170.2:n.2717G>A
ClinVar RefSeq Alternation Syntax
NR_157174.2:n.2729G>A
ClinVar RefSeq Alternation Syntax
NR_157178.2:n.2754G>A
ClinVar RefSeq Alternation Syntax
NM_001364440.2:c.*541G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2018-01-13
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000389294
ClinVar Disease
Disorders of Intracellular Cobalamin Metabolism
Observed Origin Sample
germline
Drugs