Annotation Detail

Information
Associated Genes
TREX1 ATRIP ATRIP-TREX1
Associated Variants
ATRIP c.*1442G>A, TREX1 p.Arg114His (p.R114H) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
ATRIP c.*1442G>A, TREX1 p.Arg114His (p.R114H) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
Associated Disease
Retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations
Source Database
ClinVar
Description
NM_033629.6(TREX1):c.341G>A (p.Arg114His) AND Retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations
ClinVar Allele ID
19218
ClinVar RefSeq Alternation Syntax
NM_001271023.2:c.*1442G>A
ClinVar RefSeq Alternation Syntax
NM_007248.5:c.311G>A
ClinVar RefSeq Alternation Syntax
NM_130384.3:c.*1442G>A
ClinVar RefSeq Alternation Syntax
NR_153405.1:n.3650G>A
ClinVar RefSeq Alternation Syntax
NM_033629.6:c.341G>A
ClinVar RefSeq Alternation Syntax
NM_032166.4:c.*1442G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2017-04-27
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000388382
ClinVar Disease
Retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations
Observed Origin Sample
germline
Drugs